Congenital Heart Disease

acyanotic heart disease

Acyanotic heart disease covers the congenital defects that do not, at least at first, turn a child blue. The prefix a- simply means without, so these are the without-blueness defects. Although the heart is malformed, oxygen-rich and oxygen-poor blood are not mixed in a way that lowers the oxygen delivered to the body.

Most fall into two groups: defects with a left-to-right shunt, where extra oxygenated blood is recirculated through the lungs (such as atrial and ventricular septal defects and a patent ductus arteriosus), and obstructive lesions that simply narrow a flow path (such as coarctation of the aorta or pulmonary stenosis). In all of these, blood reaching the body is still adequately oxygenated.

The label is useful but not permanent. A large left-to-right shunt left untreated for years can raise lung pressures until flow reverses, at which point an originally acyanotic defect becomes cyanotic, the transition seen in Eisenmenger syndrome.

A pink, thriving child with a murmur is found to have a small ventricular septal defect, an acyanotic heart disease that is simply monitored over time.

Many acyanotic defects are small and need only observation.

Acyanotic does not mean harmless: a large shunt or tight obstruction can still cause heart failure, growth failure, or long-term lung damage even while the child remains pink.

Also called
acyanotic congenital heart disease非青紫型先天性心脏病非青紫型先天性心臟病